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Interatrial communication

ORPHA:1478Morphological anomalyAutosomal dominant, Not applicableAdolescent, Adult, Childhood, Elderly

Фенотипы (19)

Очень частый (80–99%)2
HP:0001631Atrial septal defect
HP:0001684Secundum atrial septal defect
Частый (30–79%)2
HP:0005110Atrial fibrillation
HP:0031664Systolic heart murmur
Периодический (5–29%)13
HP:0001635Congestive heart failure
HP:0001640Cardiomegaly
HP:0001962Palpitations
HP:0002092Pulmonary arterial hypertension
HP:0002205Recurrent respiratory infections
HP:0002875Exertional dyspnea
HP:0004749Atrial flutter
HP:0005133Right ventricular dilatation
HP:0010445Primum atrial septal defect
HP:0011567Sinus venosus atrial septal defect
HP:0011712Right bundle branch block
HP:0012378Fatigue
HP:0033567Right axis deviation
Очень редкий (1–4%)2
HP:0001297Stroke
HP:0031297Unroofed coronary sinus

Эпидемиология (2)

Point prevalence
1-9 / 100 000
Europe
Point prevalence
1-5 / 10 000
Worldwide

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы