Subacute cutaneous lupus erythematosus
ORPHA:163525DiseaseAdult, Elderly
Фенотипы (HPO)19
Очень частый (80–99%)1
HP:0033555Anti-Ro/SS-A antibody positivity
Частый (30–79%)5
HP:0000992Cutaneous photosensitivity
HP:0002923Rheumatoid factor positive
HP:0003493Antinuclear antibody positivity
HP:0025526Psoriasiform lesion
HP:0025528Annular cutaneous lesion
Периодический (5–29%)10
HP:0000962Hyperkeratosis
HP:0003613Antiphospholipid antibody positivity
HP:0004334Dermal atrophy
HP:0007417Discoid lupus rash
HP:0008066Abnormal blistering of the skin
HP:0020151Anti-dsDNA antibody positivity
HP:0031540Linear IgG deposits along the epidermal basement membrane zone
HP:0031541Linear C3 deposits along the epidermal basement membrane zone
HP:0032235Anti-La/SS-B antibody positivity
HP:0033558Anti-histone antibody positivity
Очень редкий (1–4%)3
HP:0025300Malar rash
HP:0100825Cheilitis
HP:0200029Vasculitis in the skin
Эпидемиология2
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | 0.63 | United States | Value and class |
| Point prevalence | 1-9 / 100 000 | 1.4805 | United States | Value and class |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)