← Назад

Autoimmune hepatitis

ORPHA:2137DiseaseNot applicableAdolescent, Adult, Childhood, Elderly

Фенотипы (34)

Облигатный (100%)2
HP:0003237Increased circulating IgG level
HP:0010702Increased circulating antibody level
Очень частый (80–99%)7
HP:0002910Elevated circulating hepatic transaminase concentration
HP:0003262Smooth muscle antibody positivity
HP:0003453Antineutrophil antibody positivity
HP:0003493Antinuclear antibody positivity
HP:0030908Liver kidney microsome type 1 antibody positivity
HP:0030909Anti-liver cytosolic antigen type 1 antibody positivity
HP:0031925Rosette
Частый (30–79%)6
HP:0000716Depression
HP:0002027Abdominal pain
HP:0002829Arthralgia
HP:0012432Chronic fatigue
HP:0012522Spider hemangioma
HP:0032469Anti-asialoglycoprotein receptor antibody positivity
Периодический (5–29%)16
HP:0000099Glomerulonephritis
HP:0000739Anxiety
HP:0000952Jaundice
HP:0001045Vitiligo
HP:0001369Arthritis
HP:0001394Cirrhosis
HP:0001541Ascites
HP:0001744Splenomegaly
HP:0002037Inflammation of the large intestine
HP:0002239Gastrointestinal hemorrhage
HP:0003573Increased total bilirubin
HP:0006555Diffuse hepatic steatosis
HP:0030991Sclerosing cholangitis
HP:0100279Ulcerative colitis
HP:0100646Thyroiditis
HP:0200119Acute hepatitis
Очень редкий (1–4%)3
HP:0001402Hepatocellular carcinoma
HP:0004787Fulminant hepatitis
HP:0006562Viral hepatitis

Эпидемиология (17)

Point prevalence
1-5 / 10 000
Europe
Annual incidence
1-9 / 100 000
Worldwide
Point prevalence
1-5 / 10 000
Worldwide
Annual incidence
1-9 / 1 000 000
Europe
Annual incidence
1-9 / 100 000
Norway
Point prevalence
1-5 / 10 000
Norway
Annual incidence
1-9 / 1 000 000
Sweden
Point prevalence
1-5 / 10 000
New Zealand
Annual incidence
1-9 / 1 000 000
Spain
Point prevalence
1-5 / 10 000
Spain
Point prevalence
1-5 / 10 000
Sweden
Annual incidence
1-9 / 1 000 000
Israel
Point prevalence
1-5 / 10 000
Israel
Annual incidence
1-9 / 100 000
Denmark
Point prevalence
1-5 / 10 000
Denmark
Point prevalence
1-9 / 100 000
Singapore
Point prevalence
1-5 / 10 000
Specific population

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы