Idiopathic chronic eosinophilic pneumonia
ORPHA:2902DiseaseNot applicableAll ages
Фенотипы (HPO)27
Очень частый (80–99%)2
HP:0031983Abnormal pulmonary thoracic imaging finding
HP:0032177Parenchymal consolidation
Частый (30–79%)16
HP:0001047Atopic dermatitis
HP:0001974Leukocytosis
HP:0002091Restrictive ventilatory defect
HP:0002094Dyspnea
HP:0002099Asthma
HP:0002960Autoimmunity
HP:0003212Increased circulating IgE level
HP:0003565Elevated erythrocyte sedimentation rate
HP:0006516Hypersensitivity pneumonitis
HP:0011227Elevated circulating C-reactive protein concentration
HP:0012418Hypoxemia
HP:0030828Wheezing
HP:0030830Crackles
HP:0031246Nonproductive cough
HP:0032017Sputum eosinophilia
HP:0032061Hypereosinophilia
Периодический (5–29%)5
HP:0001824Weight loss
HP:0001945Fever
HP:0002829Arthralgia
HP:0025406Asthenia
HP:0030166Night sweats
Очень редкий (1–4%)4
HP:0002202Pleural effusion
HP:0011024Abnormality of the gastrointestinal tract
HP:0011354Generalized abnormality of skin
HP:0100750Atelectasis
Эпидемиология2
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only |
| Annual incidence | 1-9 / 1 000 000 | 0.23 | Iceland | Value and class |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)