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Congenital pulmonary valvar stenosis

ORPHA:3189Morphological anomalyMultigenic/multifactorial, Not applicableChildhood, Infancy, Neonatal

Фенотипы (3)

Очень частый (80–99%)1
HP:0001602Laryngeal stenosis
Частый (30–79%)1
HP:0001631Atrial septal defect
Периодический (5–29%)1
HP:0030680Abnormal cardiovascular system morphology

Эпидемиология (20)

Prevalence at birth
1-5 / 10 000
France
Prevalence at birth
1-5 / 10 000
Austria
Prevalence at birth
1-5 / 10 000
Belgium
Prevalence at birth
1-5 / 10 000
Croatia
Prevalence at birth
1-5 / 10 000
Denmark
Prevalence at birth
6-9 / 10 000
Germany
Prevalence at birth
6-9 / 10 000
Hungary
Prevalence at birth
1-9 / 100 000
Ireland
Prevalence at birth
1-5 / 10 000
Italy
Prevalence at birth
1-5 / 10 000
Malta
Prevalence at birth
1-9 / 100 000
Netherlands
Prevalence at birth
1-5 / 10 000
Norway
Prevalence at birth
1-5 / 10 000
Poland
Prevalence at birth
1-5 / 10 000
Portugal
Prevalence at birth
1-5 / 10 000
Spain
Prevalence at birth
6-9 / 10 000
Switzerland
Prevalence at birth
1-5 / 10 000
United Kingdom
Prevalence at birth
1-5 / 10 000
Ukraine
Prevalence at birth
1-5 / 10 000
Europe
Point prevalence
Unknown
Europe

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы