IgG4-related aortitis
ORPHA:449400Clinical subtypeNot applicableAdult, Elderly
Фенотипы (HPO)25
Очень частый (80–99%)2
HP:0010702Increased circulating antibody level
HP:0032300Increased circulating IgG4 level
Частый (30–79%)14
HP:0001824Weight loss
HP:0001945Fever
HP:0002027Abdominal pain
HP:0002099Asthma
HP:0002960Autoimmunity
HP:0003212Increased circulating IgE level
HP:0003419Low back pain
HP:0003493Antinuclear antibody positivity
HP:0003565Elevated erythrocyte sedimentation rate
HP:0011227Elevated circulating C-reactive protein concentration
HP:0012393Allergy
HP:0012649Increased inflammatory response
HP:0012727Thoracic aortic aneurysm
HP:0032061Hypereosinophilia
Периодический (5–29%)9
HP:0000126Hydronephrosis
HP:0002647Aortic dissection
HP:0004431Complement deficiency
HP:0004970Ascending tubular aorta aneurysm
HP:0005214Intestinal obstruction
HP:0012303Abnormal aortic arch morphology
HP:0031252Dilated left subclavian artery
HP:0032230Cytoplasmic antineutrophil antibody positivity
HP:0430021Abnormal common carotid artery morphology
Эпидемиология1
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)