Felty syndrome
ORPHA:47612DiseaseUnknownAdult
Фенотипы (HPO)36
Очень частый (80–99%)12
HP:0001367Abnormal joint morphology
HP:0001369Arthritis
HP:0001376Limitation of joint mobility
HP:0001482Subcutaneous nodule
HP:0001875Decreased total neutrophil count
HP:0002205Recurrent respiratory infections
HP:0002719Recurrent infections
HP:0002721Immunodeficiency
HP:0002797Osteolysis
HP:0002829Arthralgia
HP:0002960Autoimmunity
HP:0100769Synovitis
Частый (30–79%)10
HP:0000246Sinusitis
HP:0000389Chronic otitis media
HP:0001744Splenomegaly
HP:0001824Weight loss
HP:0001903Anemia
HP:0002716Lymphadenopathy
HP:0004332Abnormal lymphocyte morphology
HP:0006532Recurrent pneumonia
HP:0012384Rhinitis
HP:0100776Recurrent pharyngitis
Периодический (5–29%)14
HP:0000010Recurrent urinary tract infections
HP:0001701Pericarditis
HP:0001873Thrombocytopenia
HP:0002102Pleuritis
HP:0002206Pulmonary fibrosis
HP:0002240Hepatomegaly
HP:0002665Lymphoma
HP:0005528Bone marrow hypocellularity
HP:0007400Irregular hyperpigmentation
HP:0007440Generalized hyperpigmentation
HP:0009830Peripheral neuropathy
HP:0100534Episcleritis
HP:0100658Cellulitis
HP:0100806Sepsis
Эпидемиология1
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)