Pyoderma gangrenosum
ORPHA:48104DiseaseUnknownAdolescent, Adult, Childhood, Elderly
Фенотипы (HPO)15
Очень частый (80–99%)6
HP:0001945Fever
HP:0002829Arthralgia
HP:0003326Myalgia
HP:0100614Myositis
HP:0200034Papule
HP:0200042Skin ulcer
Частый (30–79%)7
HP:0001075Atrophic scars
HP:0001370Rheumatoid arthritis
HP:0002037Inflammation of the large intestine
HP:0002863Myelodysplasia
HP:0010702Increased circulating antibody level
HP:0012324Myeloid leukemia
HP:0200039Pustule
Периодический (5–29%)2
HP:0008066Abnormal blistering of the skin
HP:0200037Skin vesicle
Эпидемиология6
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Annual incidence | 1-9 / 100 000 | 1 | United States | Value and class |
| Annual incidence | 1-9 / 1 000 000 | 0.91 | United Kingdom | Value and class |
| Point prevalence | Unknown | — | Worldwide | Class only |
| Annual incidence | 1-9 / 1 000 000 | 0.33 | Spain | Value and class |
| Annual incidence | 1-9 / 1 000 000 | 0.74 | Worldwide | Value and class |
| Annual incidence | 1-9 / 1 000 000 | 0.517 | Italy | Value and class |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)