Acquired purpura fulminans
ORPHA:49566DiseaseNot applicableAdult, Childhood, Infancy, Neonatal
Фенотипы (HPO)25
Частый (30–79%)19
HP:0000988Skin rash
HP:0001063Acrocyanosis
HP:0001873Thrombocytopenia
HP:0001977Abnormal thrombosis
HP:0002958Immune dysregulation
HP:0003645Prolonged partial thromboplastin time
HP:0004855Reduced protein S activity
HP:0005521Disseminated intravascular coagulation
HP:0005543Reduced protein C activity
HP:0008066Abnormal blistering of the skin
HP:0008151Prolonged prothrombin time
HP:0011227Elevated circulating C-reactive protein concentration
HP:0011900Hypofibrinogenemia
HP:0012733Macule
HP:0025022Decreased erythrocyte sedimentation rate
HP:0025475Erythematous macule
HP:0031273Shock
HP:0031365Macular purpura
HP:0100758Gangrene
Периодический (5–29%)5
HP:0001399Hepatic failure
HP:0002170Intracranial hemorrhage
HP:0002664Neoplasm
HP:0011029Internal hemorrhage
HP:0100806Sepsis
Очень редкий (1–4%)1
HP:0025452Pyoderma gangrenosum
Эпидемиология2
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Annual incidence | Unknown | — | Worldwide | Class only |
| Point prevalence | Unknown | — | Worldwide | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)