Hepatoportal sclerosis
ORPHA:64743Histopathological subtypeAll ages
Фенотипы (HPO)30
Очень частый (80–99%)2
HP:0001744Splenomegaly
HP:0001903Anemia
Частый (30–79%)11
HP:0008151Prolonged prothrombin time
HP:0030146Abnormal liver parenchyma morphology
HP:0030169Gastric varix
HP:0031015Intrahepatic portal vein sclerosis
HP:0001409Portal hypertension
HP:0001882Leukopenia
HP:0001892Abnormal bleeding
HP:0001971Hypersplenism
HP:0002040Esophageal varix
HP:0003262Smooth muscle antibody positivity
HP:0006707Abnormality of the hepatic vasculature
Периодический (5–29%)16
HP:0000952Jaundice
HP:0000989Pruritus
HP:0001405Periportal fibrosis
HP:0001541Ascites
HP:0001873Thrombocytopenia
HP:0002239Gastrointestinal hemorrhage
HP:0002480Hepatic encephalopathy
HP:0002719Recurrent infections
HP:0002904Hyperbilirubinemia
HP:0002910Elevated circulating hepatic transaminase concentration
HP:0003073Hypoalbuminemia
HP:0011954Nodular regenerative hyperplasia of liver
HP:0020136Anticardiolipin IgG antibody positivity
HP:0020137Anticardiolipin IgM antibody positivity
HP:0030242Portal vein thrombosis
HP:0100543Cognitive impairment
Очень редкий (1–4%)1
HP:0001402Hepatocellular carcinoma
Эпидемиология1
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)