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Lymphedema with yellow nails

ORPHA:662DiseaseAdult, Childhood, Neonatal

Фенотипы (24)

Очень частый (80–99%)8
HP:0001004Lymphedema
HP:0001231Abnormal fingernail morphology
HP:0002110Bronchiectasis
HP:0003759Hypoplasia of lymphatic vessels
HP:0008388Abnormal toenail morphology
HP:0011367Yellow nails
HP:0100797Toenail dysplasia
HP:0100798Fingernail dysplasia
Частый (30–79%)6
HP:0000246Sinusitis
HP:0002094Dyspnea
HP:0002102Pleuritis
HP:0002205Recurrent respiratory infections
HP:0012384Rhinitis
HP:0012735Cough
Периодический (5–29%)10
HP:0000112Nephropathy
HP:0001806Onycholysis
HP:0002092Pulmonary arterial hypertension
HP:0002664Neoplasm
HP:0002721Immunodeficiency
HP:0009726Renal neoplasm
HP:0011354Generalized abnormality of skin
HP:0100242Sarcoma
HP:0100526Neoplasm of the lung
HP:0100574Biliary tract neoplasm

Эпидемиология (2)

Cases/families
Worldwide
Point prevalence
<1 / 1 000 000
Worldwide

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы