Immunoglobulin A vasculitis
ORPHA:761DiseaseNot applicableChildhood
Фенотипы (HPO)34
Очень частый (80–99%)10
HP:0000790Hematuria
HP:0000978Bruising susceptibility
HP:0000979Purpura
HP:0000988Skin rash
HP:0002017Nausea and vomiting
HP:0002027Abdominal pain
HP:0002633Vasculitis
HP:0002829Arthralgia
HP:0005244Gastrointestinal infarctions
HP:0200039Pustule
Частый (30–79%)10
HP:0001369Arthritis
HP:0001945Fever
HP:0002039Anorexia
HP:0002076Migraine
HP:0002383Infectious encephalitis
HP:0003326Myalgia
HP:0010783Erythema
HP:0011276Vascular skin abnormality
HP:0100796Orchitis
HP:0200042Skin ulcer
Периодический (5–29%)14
HP:0000083Renal insufficiency
HP:0000093Proteinuria
HP:0000648Optic atrophy
HP:0000969Edema
HP:0001025Urticaria
HP:0001250Seizure
HP:0001324Muscle weakness
HP:0002091Restrictive ventilatory defect
HP:0002239Gastrointestinal hemorrhage
HP:0004374Hemiplegia/hemiparesis
HP:0012733Macule
HP:0100534Episcleritis
HP:0100665Angioedema
HP:0100820Glomerulopathy
Эпидемиология8
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Annual incidence | 6-9 / 10 000 | 55.9 | Korea, Republic of | Value and class |
| Annual incidence | 1-5 / 10 000 | 30 | France | Value and class |
| Annual incidence | 1-9 / 100 000 | 6.79 | Croatia | Value and class |
| Annual incidence | 1-5 / 10 000 | 13 | United Kingdom | Value and class |
| Annual incidence | 1-9 / 100 000 | 6.1 | Netherlands | Value and class |
| Annual incidence | 1-5 / 10 000 | 17.55 | Sweden | Value and class |
| Annual incidence | 1-9 / 100 000 | 12.9 | Taiwan, Province of China | Value and class |
| Point prevalence | Unknown | — | Worldwide | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)