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Acute interstitial pneumonia

ORPHA:79126DiseaseUnknownAdult

Фенотипы (33)

Очень частый (80–99%)11
HP:0002094Dyspnea
HP:0002110Bronchiectasis
HP:0002113Pulmonary infiltrates
HP:0002878Respiratory failure
HP:0012418Hypoxemia
HP:0025177Peribronchovascular interstitial thickening
HP:0025179Ground-glass opacification on pulmonary HRCT
HP:0025392Nodular pattern on pulmonary HRCT
HP:0025393Reticulonodular pattern on pulmonary HRCT
HP:0030879Interlobular septal thickening on pulmonary HRCT
HP:0032177Parenchymal consolidation
Частый (30–79%)9
HP:0000822Hypertension
HP:0000961Cyanosis
HP:0001945Fever
HP:0002202Pleural effusion
HP:0002789Tachypnea
HP:0012378Fatigue
HP:0030830Crackles
HP:0031246Nonproductive cough
HP:0045051Decreased DLCO
Периодический (5–29%)13
HP:0001698Pericardial effusion
HP:0002206Pulmonary fibrosis
HP:0002716Lymphadenopathy
HP:0002829Arthralgia
HP:0003259Elevated circulating creatinine concentration
HP:0003326Myalgia
HP:0003565Elevated erythrocyte sedimentation rate
HP:0011227Elevated circulating C-reactive protein concentration
HP:0012398Peripheral edema
HP:0031631Subpleural honeycombing
HP:0031851Reduced hematocrit
HP:0100749Chest pain
HP:0100750Atelectasis

Эпидемиология (1)

Point prevalence
1-9 / 100 000
Europe

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы