Lymphoid interstitial pneumonia
ORPHA:79128DiseaseNot applicableAll ages
Фенотипы (HPO)34
Очень частый (80–99%)1
HP:0012735Cough
Частый (30–79%)16
HP:0000964Eczematoid dermatitis
HP:0001217Clubbing
HP:0001508Failure to thrive
HP:0002091Restrictive ventilatory defect
HP:0002094Dyspnea
HP:0002960Autoimmunity
HP:0005948Multiple pulmonary cysts
HP:0012378Fatigue
HP:0012418Hypoxemia
HP:0025179Ground-glass opacification on pulmonary HRCT
HP:0030057Autoimmune antibody positivity
HP:0030828Wheezing
HP:0030830Crackles
HP:0031691Severe viral infection
HP:0032177Parenchymal consolidation
HP:0045051Decreased DLCO
Периодический (5–29%)16
HP:0000105Enlarged kidney
HP:0000988Skin rash
HP:0001097Keratoconjunctivitis sicca
HP:0001370Rheumatoid arthritis
HP:0001824Weight loss
HP:0001945Fever
HP:0002110Bronchiectasis
HP:0002240Hepatomegaly
HP:0002721Immunodeficiency
HP:0003549Abnormality of connective tissue
HP:0011947Respiratory tract infection
HP:0025178Subpleural interstitial thickening
HP:0025180Centrilobular ground-glass opacification on pulmonary HRCT
HP:0030880Raynaud phenomenon
HP:0030950Pulmonary venous hypertension
HP:0100721Mediastinal lymphadenopathy
Очень редкий (1–4%)1
HP:0002206Pulmonary fibrosis
Эпидемиология1
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)