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Cutaneous neuroendocrine carcinoma

ORPHA:79140DiseaseNot applicableAdult, Elderly

Фенотипы (17)

Облигатный (100%)1
HP:0030447Merkel cell skin cancer
Частый (30–79%)7
HP:0000992Cutaneous photosensitivity
HP:0002730Chronic noninfectious lymphadenopathy
HP:0005374Cellular immunodeficiency
HP:0011356Regional abnormality of skin
HP:0025474Erythematous plaque
HP:0025475Erythematous macule
HP:0200036Skin nodule
Периодический (5–29%)5
HP:0002671Basal cell carcinoma
HP:0005526Lymphoid leukemia
HP:0006739Squamous cell carcinoma of the skin
HP:0006775Multiple myeloma
HP:0100570Carcinoid tumor
Очень редкий (1–4%)3
HP:0012658Abnormal brain FDG positron emission tomography
HP:0030692Brain neoplasm
HP:0040095Neoplasm of the outer ear
Исключён (0%)1
HP:0012531Pain

Эпидемиология (12)

Annual incidence
1-9 / 1 000 000
Worldwide
Point prevalence
1-9 / 100 000
Europe
Annual incidence
1-9 / 1 000 000
Europe
Lifetime Prevalence
1-9 / 1 000 000
Europe
Annual incidence
<1 / 1 000 000
Finland
Annual incidence
1-9 / 100 000
United States
Annual incidence
1-9 / 1 000 000
Denmark
Annual incidence
1-9 / 1 000 000
France
Annual incidence
1-9 / 1 000 000
United Kingdom
Annual incidence
1-9 / 100 000
Australia
Annual incidence
1-9 / 100 000
New Zealand
Annual incidence
1-9 / 100 000
Norway

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы