← Назад

Steroid-responsive encephalopathy associated with autoimmune thyroiditis

ORPHA:83601DiseaseNot applicableAll ages

Фенотипы (25)

Облигатный (100%)1
HP:0006846Acute encephalopathy
Очень частый (80–99%)2
HP:0005318Cerebral vasculitis
HP:0000872Hashimoto thyroiditis
Частый (30–79%)6
HP:0000821Hypothyroidism
HP:0000853Goiter
HP:0001289Confusion
HP:0002500Abnormal cerebral white matter morphology
HP:0002902Hyponatremia
HP:0003470Paralysis
Периодический (5–29%)14
HP:0000709Psychosis
HP:0000716Depression
HP:0000739Anxiety
HP:0001873Thrombocytopenia
HP:0001945Fever
HP:0001974Leukocytosis
HP:0002017Nausea and vomiting
HP:0002133Status epilepticus
HP:0002197Generalized-onset seizure
HP:0002315Headache
HP:0002721Immunodeficiency
HP:0007359Focal-onset seizure
HP:0009102Anterior open-bite malocclusion
HP:0012332Abnormal autonomic nervous system physiology
Очень редкий (1–4%)1
HP:0005991Limited neck flexion
Исключён (0%)1
HP:0002181Cerebral edema

Эпидемиология (1)

Point prevalence
<1 / 1 000 000
Europe

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы