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Psoriasis-related juvenile idiopathic arthritis

ORPHA:85436DiseaseUnknownAdolescent, Childhood

Фенотипы (29)

Очень частый (80–99%)1
HP:0011118Abnormality of tumor necrosis factor secretion
Частый (30–79%)12
HP:0000989Pruritus
HP:0001369Arthritis
HP:0001803Nail pits
HP:0002829Arthralgia
HP:0002960Autoimmunity
HP:0003493Antinuclear antibody positivity
HP:0003765Psoriasiform dermatitis
HP:0005764Polyarticular arthritis
HP:0031090Finger dactylitis
HP:0031091Toe dactylitis
HP:0040313Oligoarthritis
HP:0100686Enthesitis
Периодический (5–29%)11
HP:0000554Uveitis
HP:0000988Skin rash
HP:0001376Limitation of joint mobility
HP:0002815Abnormality of the knee
HP:0003019Abnormality of the wrist
HP:0003043Abnormality of the shoulder
HP:0005197Generalized morning stiffness
HP:0007663Reduced visual acuity
HP:0012122Anterior uveitis
HP:0025300Malar rash
HP:0025526Psoriasiform lesion
Очень редкий (1–4%)5
HP:0001094Iridocyclitis
HP:0001101Iritis
HP:0001806Onycholysis
HP:0010754Abnormality of the temporomandibular joint
HP:0012317Sacroiliac arthritis

Эпидемиология (1)

Point prevalence
Unknown
Worldwide

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы