Autoimmune hemolytic anemia, warm type
ORPHA:90033DiseaseMultigenic/multifactorialAll ages
Фенотипы (HPO)27
Очень частый (80–99%)6
HP:0000980Pallor
HP:0001890Autoimmune hemolytic anemia
HP:0002315Headache
HP:0002875Exertional dyspnea
HP:0002960Autoimmunity
HP:0012378Fatigue
Частый (30–79%)12
HP:0001744Splenomegaly
HP:0001923Reticulocytosis
HP:0001962Palpitations
HP:0002829Arthralgia
HP:0003641Hemoglobinuria
HP:0004835Microspherocytosis
HP:0005523Lymphoproliferative disorder
HP:0008282Unconjugated hyperbilirubinemia
HP:0020062Decreased hemoglobin concentration
HP:0020181Reduced haptoglobin level
HP:0025435Increased circulating lactate dehydrogenase concentration
HP:0032366Positive direct antiglobulin test
Периодический (5–29%)9
HP:0000952Jaundice
HP:0001635Congestive heart failure
HP:0001649Tachycardia
HP:0001945Fever
HP:0002725Systemic lupus erythematosus
HP:0005550Chronic lymphatic leukemia
HP:0012086Abnormal urinary color
HP:0030848Elevated jugular venous pressure
HP:0100749Chest pain
Эпидемиология1
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Point prevalence | 1-9 / 100 000 | — | Europe | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)