Secondary intestinal lymphangiectasia
ORPHA:90363DiseaseAdult, Elderly
Фенотипы (HPO)40
Очень частый (80–99%)2
HP:0001004Lymphedema
HP:0031686Increased stool alpha1-antitrypsin concentration
Частый (30–79%)8
HP:0000969Edema
HP:0001888Lymphopenia
HP:0002024Malabsorption
HP:0002028Chronic diarrhea
HP:0003146Hypocholesterolemia
HP:0004788Intestinal lymphedema
HP:0011741Secondary hyperaldosteronism
HP:0012378Fatigue
Периодический (5–29%)22
HP:0001394Cirrhosis
HP:0001945Fever
HP:0002013Vomiting
HP:0002202Pleural effusion
HP:0002563Constrictive pericarditis
HP:0002608Celiac disease
HP:0002665Lymphoma
HP:0002720Decreased circulating IgA level
HP:0002850Decreased circulating total IgM
HP:0002960Autoimmunity
HP:0003073Hypoalbuminemia
HP:0004313Decreased circulating antibody level
HP:0011848Abdominal colic
HP:0011900Hypofibrinogenemia
HP:0012050Anasarca
HP:0012281Chylous ascites
HP:0012537Food intolerance
HP:0031085Decreased prealbumin level
HP:0032064Gastrointestinal eosinophilia
HP:0032136Decreased circulating IgG1 level
HP:0032387Reduced transferrin level
HP:0100324Scleroderma
Очень редкий (1–4%)8
HP:0001708Right ventricular failure
HP:0001907Thromboembolism
HP:0002576Intussusception
HP:0002580Volvulus
HP:0002584Intestinal bleeding
HP:0002719Recurrent infections
HP:0005214Intestinal obstruction
HP:0012191B-cell lymphoma
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)