VIPoma
ORPHA:97282DiseaseNot applicableAll ages
Фенотипы (HPO)41
Очень частый (80–99%)3
HP:0002894Neoplasm of the pancreas
HP:0002900Hypokalemia
HP:0005208Secretory diarrhea
Частый (30–79%)15
HP:0000819Diabetes mellitus
HP:0001824Weight loss
HP:0001895Normochromic anemia
HP:0001944Dehydration
HP:0002017Nausea and vomiting
HP:0002024Malabsorption
HP:0002039Anorexia
HP:0002240Hepatomegaly
HP:0002574Episodic abdominal pain
HP:0003072Hypercalcemia
HP:0003324Generalized muscle weakness
HP:0003394Muscle spasm
HP:0004396Poor appetite
HP:0010783Erythema
HP:0012432Chronic fatigue
Периодический (5–29%)6
HP:0001046Intermittent jaundice
HP:0001406Intrahepatic cholestasis
HP:0001438Abnormality of abdomen morphology
HP:0001541Ascites
HP:0012334Extrahepatic cholestasis
HP:0030895Abnormal gastrointestinal motility
Очень редкий (1–4%)16
HP:0000820Abnormality of the thyroid gland
HP:0000837Increased circulating gonadotropin level
HP:0000845Elevated circulating growth hormone concentration
HP:0000870Increased circulating prolactin concentration
HP:0001031Subcutaneous lipoma
HP:0002747Respiratory insufficiency due to muscle weakness
HP:0002893Pituitary adenoma
HP:0002896Neoplasm of the liver
HP:0002897Parathyroid adenoma
HP:0003005Ganglioneuroma
HP:0003118Increased circulating cortisol level
HP:0003528Elevated calcitonin
HP:0006719Benign gastrointestinal tract tumors
HP:0006731Follicular thyroid carcinoma
HP:0008200Primary hyperparathyroidism
HP:0008256Adrenocortical adenoma
Исключён (0%)1
HP:0002573Hematochezia
Эпидемиология2
| Тип оценки | Класс распространённости | Среднее (на 100к) | Регион | Квалификация |
|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | — | Europe | Class only |
| Point prevalence | <1 / 1 000 000 | — | Europe | Class only |
Лекарства и терапия
Источник: Open Targets Platform (в реальном времени)
Клинические исследования
Источник: ClinicalTrials.gov (в реальном времени)