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Herpes simplex virus encephalitis

ORPHA:1930DiseaseMultigenic/multifactorial, Not applicableAll ages

Ассоциированные гены (5)

UNC93B1
unc-93B1 regulator of TLR signaling
Major susceptibility factor in
OMIM: 608204
TLR3
toll like receptor 3
Major susceptibility factor in
OMIM: 603029
TICAM1
TIR domain containing adaptor molecule 1
Major susceptibility factor in
OMIM: 607601
TRAF3
TNF receptor associated factor 3
Major susceptibility factor in
OMIM: 601896
TBK1
TANK binding kinase 1
Major susceptibility factor in
OMIM: 604834

Фенотипы (30)

Очень частый (80–99%)4
HP:0002353EEG abnormality
HP:0004372Reduced consciousness/confusion
HP:0012443Abnormality of brain morphology
HP:0200149CSF lymphocytic pleiocytosis
Частый (30–79%)13
HP:0001250Seizure
HP:0001945Fever
HP:0001974Leukocytosis
HP:0002017Nausea and vomiting
HP:0002167Abnormality of speech or vocalization
HP:0002315Headache
HP:0002902Hyponatremia
HP:0002922Increased CSF protein concentration
HP:0004887Respiratory failure requiring assisted ventilation
HP:0007185Loss of consciousness
HP:0011897Neutrophilia
HP:0012378Fatigue
HP:0031179Nuchal rigidity
Периодический (5–29%)13
HP:0001259Coma
HP:0001262Excessive daytime somnolence
HP:0001347Hyperreflexia
HP:0002133Status epilepticus
HP:0002181Cerebral edema
HP:0002349Focal aware seizure
HP:0002384Focal impaired awareness seizure
HP:0002721Immunodeficiency
HP:0004302Functional motor deficit
HP:0011227Elevated circulating C-reactive protein concentration
HP:0011972Hypoglycorrhachia
HP:0025143Chills
HP:0030955Alcoholism

Эпидемиология (4)

Annual incidence
1-9 / 1 000 000
Worldwide
Annual incidence
1-9 / 1 000 000
United Kingdom
Annual incidence
1-9 / 1 000 000
United States
Point prevalence
Unknown
Europe

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы