← Назад

Arginine vasopressin resistance

ORPHA:223DiseaseAutosomal dominant, Autosomal recessive, X-linked recessiveInfancy, Neonatal

Ассоциированные гены (2)

AVPR2
arginine vasopressin receptor 2
Disease-causing germline mutation(s) in
OMIM: 300538
AQP2
aquaporin 2
Disease-causing germline mutation(s) in
OMIM: 107777

Фенотипы (21)

Облигатный (100%)1
HP:0009806Nephrogenic diabetes insipidus
Очень частый (80–99%)3
HP:0003158Hyposthenuria
HP:0003228Hypernatremia
HP:0004906Hypernatremic dehydration
Частый (30–79%)6
HP:0001508Failure to thrive
HP:0001945Fever
HP:0001959Polydipsia
HP:0002017Nausea and vomiting
HP:0002019Constipation
HP:0002039Anorexia
Периодический (5–29%)8
HP:0004322Short stature
HP:0011106Hypovolemia
HP:0011968Feeding difficulties
HP:0000009Functional abnormality of the bladder
HP:0000072Hydroureter
HP:0000083Renal insufficiency
HP:0001250Seizure
HP:0001510Growth delay
Очень редкий (1–4%)3
HP:0001263Global developmental delay
HP:0001561Polyhydramnios
HP:0010677Enuresis nocturna

Эпидемиология (2)

Point prevalence
1-9 / 1 000 000
Europe
Prevalence at birth
1-9 / 1 000 000
Specific population

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы