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Familial papillary or follicular thyroid carcinoma

ORPHA:319487DiseaseNot applicableAdult

Ассоциированные гены (3)

MINPP1
multiple inositol-polyphosphate phosphatase 1
Candidate gene tested in
OMIM: 605391
FOXE1
forkhead box E1
Disease-causing germline mutation(s) in
OMIM: 602617
HABP2
hyaluronan binding protein 2
Disease-causing germline mutation(s) in
OMIM: 603924

Фенотипы (15)

Очень частый (80–99%)4
HP:0005994Nodular goiter
HP:0006731Follicular thyroid carcinoma
HP:0012288Neoplasm of head and neck
HP:3000037Abnormality of neck blood vessel
Частый (30–79%)3
HP:0000853Goiter
HP:0002730Chronic noninfectious lymphadenopathy
HP:0002733Abnormality of the lymph nodes
Периодический (5–29%)8
HP:0002176Spinal cord compression
HP:0002653Bone pain
HP:0002757Recurrent fractures
HP:0002895Papillary thyroid carcinoma
HP:0003003Colon cancer
HP:0006528Chronic lung disease
HP:0006766Papillary renal cell carcinoma
HP:0012531Pain

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы