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Common arterial trunk

ORPHA:3384Morphological anomalyNot applicableInfancy, Neonatal

Ассоциированные гены (2)

NKX2-6
NK2 homeobox 6
Major susceptibility factor in
OMIM: 611770
PLXND1
plexin D1
Disease-causing germline mutation(s) in
OMIM: 604282

Фенотипы (36)

Облигатный (100%)1
HP:0001660Truncus arteriosus
Очень частый (80–99%)5
HP:0000961Cyanosis
HP:0001627Abnormal heart morphology
HP:0001649Tachycardia
HP:0001654Abnormal heart valve morphology
HP:0031653Abnormal heart valve physiology
Частый (30–79%)8
HP:0001511Intrauterine growth retardation
HP:0001629Ventricular septal defect
HP:0001640Cardiomegaly
HP:0001659Aortic regurgitation
HP:0001667Right ventricular hypertrophy
HP:0002789Tachypnea
HP:0011660Anomalous origin of one pulmonary artery from ascending aorta
HP:0012020Right aortic arch
Периодический (5–29%)19
HP:0000778Hypoplasia of the thymus
HP:0000849Adrenocortical abnormality
HP:0001631Atrial septal defect
HP:0001636Tetralogy of Fallot
HP:0001642Pulmonic stenosis
HP:0001643Patent ductus arteriosus
HP:0001999Abnormal facial shape
HP:0002089Pulmonary hypoplasia
HP:0002101Abnormal lung lobation
HP:0004415Pulmonary artery stenosis
HP:0004935Pulmonary artery atresia
HP:0005301Persistent left superior vena cava
HP:0006704Abnormal coronary artery morphology
HP:0011611Interrupted aortic arch
HP:0011640Single coronary artery origin
HP:0025575Abnormal superior vena cava morphology
HP:0031014Arteria lusoria
HP:0045060Aplasia/hypoplasia involving bones of the extremities
HP:0100598Pulmonary edema
Очень редкий (1–4%)3
HP:0001669Transposition of the great arteries
HP:0004971Pulmonary artery hypoplasia
HP:0031635Anomalous origin of the left common carotid artery from the brachiocephalic artery

Эпидемиология (16)

Prevalence at birth
1-9 / 100 000
Worldwide
Prevalence at birth
1-9 / 100 000
Europe
Prevalence at birth
1-9 / 100 000
Belgium
Prevalence at birth
1-9 / 100 000
France
Prevalence at birth
1-9 / 100 000
Germany
Prevalence at birth
1-9 / 100 000
Hungary
Prevalence at birth
1-9 / 100 000
Ireland
Prevalence at birth
1-9 / 100 000
Italy
Prevalence at birth
1-9 / 100 000
Netherlands
Prevalence at birth
1-9 / 100 000
Norway
Prevalence at birth
1-9 / 100 000
Poland
Prevalence at birth
1-9 / 100 000
Spain
Prevalence at birth
1-5 / 10 000
Switzerland
Prevalence at birth
1-9 / 100 000
United Kingdom
Prevalence at birth
1-9 / 100 000
Ukraine
Point prevalence
Unknown
Worldwide

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы