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Fibrolamellar hepatocellular carcinoma

ORPHA:401920DiseaseNot applicableAdolescent, Adult

Ассоциированные гены (2)

DNAJB1
DnaJ heat shock protein family (Hsp40) member B1
Part of a fusion gene in
OMIM: 604572
PRKACA
protein kinase cAMP-activated catalytic subunit alpha
Part of a fusion gene in
OMIM: 601639

Эпидемиология (22)

Annual incidence
<1 / 1 000 000
United States
Annual incidence
<1 / 1 000 000
Austria
Annual incidence
<1 / 1 000 000
Belgium
Annual incidence
<1 / 1 000 000
Bulgaria
Annual incidence
<1 / 1 000 000
Czech Republic
Annual incidence
<1 / 1 000 000
Estonia
Annual incidence
<1 / 1 000 000
Finland
Annual incidence
<1 / 1 000 000
France
Annual incidence
<1 / 1 000 000
Germany
Annual incidence
<1 / 1 000 000
Iceland
Annual incidence
<1 / 1 000 000
Ireland
Annual incidence
1-9 / 1 000 000
Italy
Annual incidence
<1 / 1 000 000
Latvia
Annual incidence
<1 / 1 000 000
Norway
Annual incidence
<1 / 1 000 000
Poland
Annual incidence
<1 / 1 000 000
Portugal
Annual incidence
<1 / 1 000 000
Slovakia
Annual incidence
<1 / 1 000 000
Spain
Annual incidence
<1 / 1 000 000
Switzerland
Annual incidence
<1 / 1 000 000
Netherlands
Annual incidence
<1 / 1 000 000
United Kingdom
Annual incidence
<1 / 1 000 000
Europe

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы