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Autosomal dominant hypocalcemia

ORPHA:428Clinical subtypeAutosomal dominantAll ages

Ассоциированные гены (2)

CASR
calcium sensing receptor
Disease-causing germline mutation(s) (gain of function) in
OMIM: 601199
GNA11
G protein subunit alpha 11
Disease-causing germline mutation(s) (gain of function) in
OMIM: 139313

Фенотипы (30)

Очень частый (80–99%)11
HP:0000708Atypical behavior
HP:0000712Emotional lability
HP:0000716Depression
HP:0000739Anxiety
HP:0002150Hypercalciuria
HP:0002356Writer's cramp
HP:0002901Hypocalcemia
HP:0003401Paresthesia
HP:0003457EMG abnormality
HP:0003473Fatigable weakness
HP:0040148Cortical myoclonus
Частый (30–79%)12
HP:0000121Nephrocalcinosis
HP:0000958Dry skin
HP:0001231Abnormal fingernail morphology
HP:0001596Alopecia
HP:0001597Abnormality of the nail
HP:0002027Abdominal pain
HP:0002615Hypotension
HP:0002793Abnormal pattern of respiration
HP:0002905Hyperphosphatemia
HP:0002917Hypomagnesemia
HP:0011675Arrhythmia
HP:0012608Hypermagnesiuria
Периодический (5–29%)7
HP:0000648Optic atrophy
HP:0000964Eczematoid dermatitis
HP:0001635Congestive heart failure
HP:0002516Increased intracranial pressure
HP:0004349Reduced bone mineral density
HP:0004372Reduced consciousness/confusion
HP:0007400Irregular hyperpigmentation

Эпидемиология (3)

Point prevalence
1-9 / 1 000 000
Denmark
Point prevalence
Unknown
Worldwide
Point prevalence
1-9 / 100 000
United States

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы