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Female infertility due to oocyte meiotic arrest

ORPHA:488191DiseaseAutosomal recessiveAdolescent, Adult

Ассоциированные гены (6)

TLE6
TLE family member 6, subcortical maternal complex member
Disease-causing germline mutation(s) in
OMIM: 612399
ZFP36L2
ZFP36 like 2 zinc finger CCCH-type
Disease-causing germline mutation(s) in
OMIM: 612053
WEE2
WEE2 oocyte meiosis inhibiting kinase
Disease-causing germline mutation(s) (loss of function) in
OMIM: 614084
PANX1
pannexin 1
Disease-causing germline mutation(s) (gain of function) in
OMIM: 608420
PATL2
PAT1 homolog 2
Disease-causing germline mutation(s) (loss of function) in
OMIM: 614661
TUBB8
tubulin beta 8 class VIII
Disease-causing germline mutation(s) in
OMIM: 616768

Фенотипы (6)

Облигатный (100%)2
HP:0008222Female infertility
HP:0031515Abnormal meiosis
Частый (30–79%)1
HP:0031516Oocyte arrest at metaphase I
Периодический (5–29%)1
HP:0020155Abnormal oocyte morphology
Исключён (0%)2
HP:0000147Polycystic ovaries
HP:0008669Abnormal spermatogenesis

Эпидемиология (2)

Cases/families
Worldwide
Point prevalence
Unknown
Worldwide

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы