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Sarcoidosis

ORPHA:797DiseaseMultigenic/multifactorialAdolescent, Adult, Childhood, Elderly

Ассоциированные гены (2)

BTNL2
butyrophilin like 2
Major susceptibility factor in
OMIM: 606000
HLA-DRB1
major histocompatibility complex, class II, DR beta 1
Major susceptibility factor in
OMIM: 142857

Фенотипы (77)

Частый (30–79%)19
HP:0000554Uveitis
HP:0001386Joint swelling
HP:0001410Decreased liver function
HP:0001824Weight loss
HP:0001873Thrombocytopenia
HP:0001882Leukopenia
HP:0001945Fever
HP:0002088Abnormal lung morphology
HP:0002094Dyspnea
HP:0002103Abnormality of the pleura
HP:0002202Pleural effusion
HP:0003011Abnormality of the musculature
HP:0011121Abnormal skin morphology
HP:0012219Erythema nodosum
HP:0012378Fatigue
HP:0012735Cough
HP:0100749Chest pain
HP:0100828Increased T cell count
HP:0200036Skin nodule
Периодический (5–29%)51
HP:0000518Cataract
HP:0000618Blindness
HP:0000620Dacryocystitis
HP:0000787Nephrolithiasis
HP:0000873Diabetes insipidus
HP:0000953Hyperpigmentation of the skin
HP:0001010Hypopigmentation of the skin
HP:0001097Keratoconjunctivitis sicca
HP:0001369Arthritis
HP:0001399Hepatic failure
HP:0001409Portal hypertension
HP:0001482Subcutaneous nodule
HP:0001596Alopecia
HP:0001903Anemia
HP:0001970Tubulointerstitial nephritis
HP:0002097Emphysema
HP:0002107Pneumothorax
HP:0002110Bronchiectasis
HP:0002150Hypercalciuria
HP:0002206Pulmonary fibrosis
HP:0002240Hepatomegaly
HP:0002716Lymphadenopathy
HP:0002733Abnormality of the lymph nodes
HP:0002781Upper airway obstruction
HP:0002921Abnormality of the cerebrospinal fluid
HP:0002922Increased CSF protein concentration
HP:0003072Hypercalcemia
HP:0003701Proximal muscle weakness
HP:0004756Ventricular tachycardia
HP:0007734Enlarged lacrimal glands
HP:0009830Peripheral neuropathy
HP:0010310Chylothorax
HP:0010628Facial palsy
HP:0011024Abnormality of the gastrointestinal tract
HP:0011675Arrhythmia
HP:0011801Enlargement of parotid gland
HP:0011850Parotitis
HP:0012062Bone cyst
HP:0012243Abnormal reproductive system morphology
HP:0012722Heart block
HP:0030146Abnormal liver parenchyma morphology
HP:0030872Abnormal cardiac ventricular function
HP:0033505Livedo reticularis
HP:0040186Maculopapular exanthema
HP:0100699Scarring
HP:0200035Skin plaque
HP:0000083Renal insufficiency
HP:0000121Nephrocalcinosis
HP:0000433Abnormality of the nasal mucosa
HP:0000501Glaucoma
HP:0000502Abnormal conjunctiva morphology
Очень редкий (1–4%)7
HP:0000836Hyperthyroidism
HP:0001878Hemolytic anemia
HP:0001880Eosinophilia
HP:0002045Hypothermia
HP:0002105Hemoptysis
HP:0000821Hypothyroidism
HP:0000834Abnormality of the adrenal glands

Эпидемиология (34)

Point prevalence
6-9 / 10 000
United States
Point prevalence
1-5 / 10 000
Worldwide
Point prevalence
1-5 / 10 000
Ireland
Annual incidence
1-9 / 100 000
Croatia
Point prevalence
1-5 / 10 000
Europe
Annual incidence
1-9 / 100 000
United Kingdom
Point prevalence
1-5 / 10 000
France
Annual incidence
1-9 / 100 000
Spain
Point prevalence
1-5 / 10 000
Finland
Annual incidence
1-9 / 100 000
Denmark
Annual incidence
1-9 / 100 000
Switzerland
Point prevalence
6-9 / 10 000
Switzerland
Annual incidence
1-9 / 100 000
Greece
Point prevalence
1-9 / 100 000
Greece
Annual incidence
1-9 / 100 000
Iceland
Annual incidence
1-9 / 100 000
Czech Republic
Point prevalence
6-9 / 10 000
Czech Republic
Annual incidence
1-9 / 100 000
Australia
Annual incidence
1-9 / 100 000
Japan
Point prevalence
1-9 / 100 000
Japan
Annual incidence
1-9 / 1 000 000
Korea, Republic of
Annual incidence
1-9 / 1 000 000
Singapore
Point prevalence
1-5 / 10 000
Italy
Annual incidence
1-9 / 100 000
France
Point prevalence
>1 / 1000
Sweden
Annual incidence
1-5 / 10 000
Sweden
Point prevalence
1-9 / 100 000
Taiwan, Province of China
Point prevalence
1-9 / 1 000 000
Portugal
Point prevalence
1-5 / 10 000
Norway
Annual incidence
1-5 / 10 000
Norway
Point prevalence
1-5 / 10 000
Canada
Point prevalence
1-5 / 10 000
Guadeloupe
Annual incidence
1-9 / 100 000
Guadeloupe
Annual incidence
1-9 / 1 000 000
Uruguay

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы