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Microtia

ORPHA:83463Morphological anomalyAutosomal dominant, Autosomal recessive, Not applicableInfancy, Neonatal

Ассоциированные гены (1)

HOXA2
homeobox A2
Disease-causing germline mutation(s) in
OMIM: 604685

Фенотипы (9)

Облигатный (100%)1
HP:0008551Microtia
Очень частый (80–99%)1
HP:0040119Unilateral conductive hearing impairment
Частый (30–79%)5
HP:0000377Abnormal pinna morphology
HP:0000413Atresia of the external auditory canal
HP:0000750Delayed speech and language development
HP:0008589Hypoplastic helices
HP:0009892Anotia
Периодический (5–29%)2
HP:0001360Holoprosencephaly
HP:0007018Attention deficit hyperactivity disorder

Эпидемиология (17)

Point prevalence
1-5 / 10 000
Specific population
Prevalence at birth
1-5 / 10 000
Europe
Point prevalence
1-5 / 10 000
Europe
Prevalence at birth
1-5 / 10 000
Worldwide
Point prevalence
1-5 / 10 000
Worldwide
Prevalence at birth
1-9 / 100 000
France
Point prevalence
1-9 / 100 000
France
Prevalence at birth
1-9 / 100 000
Italy
Point prevalence
1-9 / 100 000
Italy
Prevalence at birth
1-9 / 100 000
Sweden
Point prevalence
1-9 / 100 000
Sweden
Prevalence at birth
1-5 / 10 000
United States
Point prevalence
1-5 / 10 000
United States
Prevalence at birth
1-5 / 10 000
Finland
Point prevalence
1-5 / 10 000
Finland
Prevalence at birth
>1 / 1000
Ecuador
Prevalence at birth
6-9 / 10 000
Chile

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы