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Congenital or early infantile CACH syndrome

ORPHA:157713Clinical subtypeAutosomal recessiveInfancy, Neonatal

Ассоциированные гены (5)

EIF2B1
eukaryotic translation initiation factor 2B subunit alpha
Disease-causing germline mutation(s) in
OMIM: 606686
EIF2B2
eukaryotic translation initiation factor 2B subunit beta
Disease-causing germline mutation(s) in
OMIM: 606454
EIF2B3
eukaryotic translation initiation factor 2B subunit gamma
Disease-causing germline mutation(s) in
OMIM: 606273
EIF2B4
eukaryotic translation initiation factor 2B subunit delta
Disease-causing germline mutation(s) in
OMIM: 606687
EIF2B5
eukaryotic translation initiation factor 2B subunit epsilon
Disease-causing germline mutation(s) in
OMIM: 603945

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы