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Hereditary atrial fibrillation

ORPHA:334DiseaseAutosomal dominantAdult, Elderly

Ассоциированные гены (24)

ABCC9
ATP binding cassette subfamily C member 9
Candidate gene tested in
OMIM: 601439
PITX2
paired like homeodomain 2
Disease-causing germline mutation(s) (loss of function) in
OMIM: 601542
SCN5A
sodium voltage-gated channel alpha subunit 5
Disease-causing germline mutation(s) (gain of function) in
OMIM: 600163
GATA4
GATA binding protein 4
Disease-causing germline mutation(s) (loss of function) in
OMIM: 600576
KCNE1
potassium voltage-gated channel subfamily E regulatory subunit 1
Candidate gene tested in
OMIM: 176261
KCNE2
potassium voltage-gated channel subfamily E regulatory subunit 2
Disease-causing germline mutation(s) (gain of function) in
OMIM: 603796
KCNJ2
potassium inwardly rectifying channel subfamily J member 2
Disease-causing germline mutation(s) (gain of function) in
OMIM: 600681
KCNQ1
potassium voltage-gated channel subfamily Q member 1
Disease-causing germline mutation(s) (gain of function) in
OMIM: 607542
NKX2-5
NK2 homeobox 5
Disease-causing germline mutation(s) (loss of function) in
OMIM: 600584
GJA5
gap junction protein alpha 5
Disease-causing germline mutation(s) in
OMIM: 121013
SCN1B
sodium voltage-gated channel beta subunit 1
Candidate gene tested in
OMIM: 600235
KCNJ3
potassium inwardly rectifying channel subfamily J member 3
Disease-causing germline mutation(s) in
OMIM: 601534
MYL4
myosin light chain 4
Disease-causing germline mutation(s) in
OMIM: 160770
TTN
titin
Major susceptibility factor in
OMIM: 188840
NKX2-6
NK2 homeobox 6
Major susceptibility factor in
OMIM: 611770
SCN4B
sodium voltage-gated channel beta subunit 4
Disease-causing germline mutation(s) in
OMIM: 608256
KCNA5
potassium voltage-gated channel subfamily A member 5
Disease-causing germline mutation(s) (loss of function) in
OMIM: 176267
NUP155
nucleoporin 155
Disease-causing germline mutation(s) (loss of function) in
OMIM: 606694
NPPA
natriuretic peptide A
Disease-causing germline mutation(s) in
OMIM: 108780
SCN3B
sodium voltage-gated channel beta subunit 3
Disease-causing germline mutation(s) (loss of function) in
OMIM: 608214
GATA6
GATA binding protein 6
Disease-causing germline mutation(s) (loss of function) in
OMIM: 601656
GATA5
GATA binding protein 5
Disease-causing germline mutation(s) (loss of function) in
OMIM: 611496
SCN2B
sodium voltage-gated channel beta subunit 2
Disease-causing germline mutation(s) (loss of function) in
OMIM: 601327
KCNJ5
potassium inwardly rectifying channel subfamily J member 5
Disease-causing germline mutation(s) in
OMIM: 600734

Фенотипы (11)

Частый (30–79%)8
HP:0001279Syncope
HP:0001962Palpitations
HP:0002094Dyspnea
HP:0002321Vertigo
HP:0003546Exercise intolerance
HP:0005110Atrial fibrillation
HP:0012378Fatigue
HP:0100749Chest pain
Периодический (5–29%)3
HP:0001658Myocardial infarction
HP:0001727Thromboembolic stroke
HP:0001907Thromboembolism

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы