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Atypical hemolytic uremic syndrome with complement gene abnormality

ORPHA:544472Etiological subtypeAll ages

Ассоциированные гены (6)

THBD
thrombomodulin
Candidate gene tested in
OMIM: 188040
C3
complement C3
Disease-causing germline mutation(s) in
OMIM: 120700
CD46
CD46 molecule
Disease-causing germline mutation(s) in
OMIM: 120920
CFB
complement factor B
Disease-causing germline mutation(s) in
OMIM: 138470
CFH
complement factor H
Disease-causing germline mutation(s) in
OMIM: 134370
CFI
complement factor I
Disease-causing germline mutation(s) in
OMIM: 217030

Эпидемиология (1)

Point prevalence
Unknown
Europe

Лекарства и терапия

Источник: Open Targets Platform (в реальном времени)

Клинические исследования

Источник: ClinicalTrials.gov (в реальном времени)

Внешние ресурсы