MEDLIB
Orphanet Database

Редкие заболевания

7,547 заболеваний с генами, фенотипами и эпидемиологией

7,547Болезней
4 552Генов
8 700Фенотипов

X-linked intellectual disability-hypogonadism-ichthyosis-obesity-short stature syndrome

ORPHA:3055Мальформация
X-linked recessive

X-linked intellectual disability-hypotonia-facial dysmorphism-aggressive behavior syndrome

ORPHA:85329Мальформация
X-linked recessive

X-linked intellectual disability-hypotonia-movement disorder syndrome

ORPHA:457260Заболевание
X-linked dominant

X-linked intellectual disability-limb spasticity-retinal dystrophy-arginine vasopressin deficiency

ORPHA:423479Заболевание
X-linked recessive

X-linked intellectual disability-macrocephaly-macroorchidism syndrome

ORPHA:85320Мальформация
X-linked recessive

X-linked intellectual disability-plagiocephaly syndrome

ORPHA:2898Мальформация
X-linked recessive

X-linked intellectual disability-psychosis-macroorchidism syndrome

ORPHA:3077Мальформация
X-linked dominant

X-linked intellectual disability-retinitis pigmentosa syndrome

ORPHA:85332Заболевание
X-linked recessive

X-linked intellectual disability-seizures-psoriasis syndrome

ORPHA:3052Заболевание
X-linked recessive

X-linked intellectual disability-short stature-overweight syndrome

ORPHA:457240Мальформация
X-linked recessive

X-linked keloid scarring-reduced joint mobility-increased optic cup-to-disc ratio syndrome

ORPHA:482606Мальформация
X-linked recessive

X-linked lethal multiple pterygium syndrome

ORPHA:79447Мальформация
X-linked dominant, X-linked recessive

X-linked lissencephaly with abnormal genitalia

ORPHA:452Мальформация
X-linked recessive

X-linked lymphoproliferative disease

ORPHA:2442Клин. группа
X-linked recessive

X-linked lymphoproliferative disease due to SAP deficiency

ORPHA:538931Заболевание
X-linked recessive

X-linked lymphoproliferative disease due to XIAP deficiency

ORPHA:538934Заболевание
X-linked recessive

X-linked mandibulofacial dysostosis

ORPHA:1131Мальформация
X-linked recessive

X-linked mendelian susceptibility to mycobacterial diseases

ORPHA:319605Заболевание
X-linked recessive

X-linked microcephaly-growth retardation-prognathism-cryptorchidism syndrome

ORPHA:435938Мальформация
X-linked recessive

X-linked myopathy with excessive autophagy

ORPHA:25980Заболевание
X-linked recessive

X-linked myopathy with postural muscle atrophy

ORPHA:178461Заболевание
X-linked recessive

X-linked myotubular myopathy-abnormal genitalia syndrome

ORPHA:456328Заболевание
Unknown

X-linked neurodegenerative syndrome, Bertini type

ORPHA:85334Заболевание
X-linked recessive

X-linked neurodegenerative syndrome, Hamel type

ORPHA:85336Заболевание
X-linked recessive